An Unusual Case of Hepatosplenomegaly
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منابع مشابه
An Unusual Case of Hepatosplenomegaly with Cytopenia
Autoimmune lymphoproliferative syndrome (ALPS) is a rare, inherited disorder of immune dysregulation secondary to defective lymphocyte apoptosis. This leads to uninhibited proliferation of lymphoid tissue manifesting with lymphadenopathy, hepatosplenomegaly, autoimmune cytopenia, and an increased risk of lymphoid malignancy. We report a 2 year old boy with fever, generalized lymphadenopathy, he...
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تاریخ انتشار 2012